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KMID : 0882420110810060786
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Korean Journal of Medicine
2011 Volume.81 No. 6 p.786 ~ p.791
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Two Cases of Neuroendocrine Carcinoma and GIST in a Patient with Neurofibromatosis Type 1
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Choi Won-Young
Hong Seung-Dok
Kim Ha-Na
Hwang Jun-Eul
Shim Hyun-Jeong
Bae Woo-Kyun
Choi Yoo-Duk
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Abstract
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Patients with neurofibromatosis type 1 (NF1) are at increased risk of developing tumors throughout the gastrointestinal tract, including neuromas, gastrointestinal stromal tumors (GISTs), and periampullary somatostatin-rich carcinoids. The simultaneous occurrence of a GIST and a well-differentiated neuroendocrine carcinoma in a patient with NF1 is very rare. Here, we report two cases of the coexistence of a low-risk GIST in the jejunum with a well-differentiated neuroendocrine carcinoma in the duodenum in patients with NF1. These cases strengthen the known association of GIST with neuroendocrine carcinoma in patients with NF1.
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KEYWORD
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Neurofibromatosis type 1, Gastrointestinal stromal tumor, Neuroendocrine carcinoma
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